Abstract

BLANCO, Maitena et al. Desmoplastic round cell tumor. Medicina (B. Aires) [online]. 2023, vol.83, n.4, pp.612-616. ISSN 0025-7680.

Desmoplastic small round cell tumor is a rare and very aggressive neoplasm that belongs to the family of “small round blue cell tumors”. It has a higher incidence in males in the second decade of life. It is due to trans location t(11;22) (p13;q12). It can be located both in the abdomen and in the retroperitoneum and is character ized by nonspecific symptoms. The treatment is very varied and the one that guarantees the total cure of the patient has not yet been detected.

The objective of this study is to expose a clinical case of desmoplastic tumor as an rare abdominal disease and its imaging expression.

Keywords : Desmoplastic small round cell tumor; Retroperitoneum; Gene translocation.

        · abstract in Spanish     · text in Spanish     · Spanish ( pdf )