Abstract

SANCHEZ, María Vázquez et al. Linear morphea in saber coup: about a case. Arch. argent. pediatr. [online]. 2022, vol.120, n.2, pp.13-13.  Epub Apr 01, 2022. ISSN 0325-0075.  http://dx.doi.org/10.5546/aap.2022.e75.

Linear morphea in coup de sabre is a dermatological entity characterized by progressive, sclerosing inflammation of the skin tissue in the frontal region and on the scalp. Headache and seizures are two of the most frequent extracutaneous symptoms and they are caused by the growth of the lesion towards underlying structures. An early diagnosis is important to stop cranial progression and try to avoid secondary complications, mainly neurological. The diagnosis is relied on compatible clinical signs and a pathological study that allows a definitive confirmation. The treatment of choice is combination therapy with oral corticosteroids and methotrexate. Despite an adequate pharmacological treatment, this pathology can present a recurrent course and cause long-term sequelae. We present the case of a girl who was diagnosed quickly, despite a not very noticeable symptoms. She has been treated with oral methotrexate with a good response, without side effects.

Keywords : morphea; localized scleroderma; pediatrics; dermatology.

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