Abstract

VELAZCO, María P et al. Noncompaction of the Ventricular Myocardium and Hereditary Spherocytosis: A Case Report. Rev. argent. cardiol. [online]. 2008, vol.76, n.1, pp.67-69. ISSN 1850-3748.

Noncompaction of the ventricular myocardium is a congenital disorder that has been categorized as an unclassified cardiomyopathy. The association of this congenital cardiomyopathy with hereditary spherocytosis has been published only once. In this case report, a woman with a history of hereditary spherocytosis was admitted to our Coronary Care Unit with heart failure due to dilated cardiomyopathy. The echocardiogram showed a mobile and hyperechogenic image and, subsequently, a cardiovascular magnetic resonance imaging was performed, resulting in a diagnosis of noncompaction of the ventricular myocardium. The patient was transferred to a Tertiary Medical Center for cardiac transplantation, but she died before it could be carried out.

Keywords : Cardiomyopathy; Hereditary Spherocytosis; Magnetic Resonance.

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