Abstract

TARRAB SALEM, GV; COPPOLA, M; HAAS, E  and  MOSTO, A. Stewart-Treves Syndrome. Rev. argent. dermatol. [online]. 2016, vol.97, n.2, pp.74-83. ISSN 1851-300X.

The Stewart-Treves Syndrome is a rare cutaneous angiosarcoma, that occurs in patients with chronic lymphedema. It is classically described after performing radical mastectomy with lymph node dissection and/or radiation therapy. Its mortality is high. We have reported the case of a 76 years old patient, who underwent radical mastectomy with axillary lymph node dissection, followed by chemotherapy and radiotherapy. She came 13 years later with an intense pain and exophytic, ulcerated, angiomatous, bleeding and smelly tumor injury in front side of the left arm. She had an edema of the left upper limb with several years of evolution. After performing punch biopsy of the lesion the histopathological results were compatible with lymphangiosarcoma. The family, jointly with the surgery service decided to remove the tumor with limb preservation. She died 11 months after the diagnosis of Stewart-Treves syndrome, performed in our department.

Keywords : Radical mastectomy; Lymphangiosarcoma; Stewart-Treves Syndrome; Chronic lymphedema; Axillary lymph node dissection.