Abstract

DUMAS, L et al. Pediatric mastocytosis: report of 23 cases in 5 years. Rev. argent. dermatol. [online]. 2019, vol.100, n.2, pp.41-50. ISSN 1851-300X.

Introduction: Mastocytosis is a heterogeneous group of disorders, characterized by a proliferation of mast cells and its accumulation in several organs, being the skin the most frequently affected one.

Design: A descriptive, retrospective cross-sectional study, was conducted in the period from April 2013 to March 2018 in Neuquen city.

Materials and Method: Electronic medical records of patients diagnosed with cutaneous mastocytosis who attended to the pediatric dermatology clinic in Neuquen city were reviewed.

Results: We present 23 cases of cutaneous mastocytosis, of which 60,87% were maculopapular and 39,13% mastocytomas. There were no significant differences in terms of sexes. Most of them presented localized lesions in trunk and limbs. 95% had positive Darier´s sign.

Conclusions: In our sample, the most frequent clinical presentation was maculopapular mastocytosis, and the age of onset was during the first year of life in all patients. The majority of lesions were distributed over the trunk and limbs. Patients with mastocytoma remained stable; maculopapular patients recieved antihistamines, with good evolution.

Keywords : antihistamines.