Abstract

SARDOY, A et al. PITIRIASIS RUBRA PILARIS CLÁSICA DEL ADULTO: UNA PATOLOGÍA POCO FRECUENTE. Rev. argent. dermatol. [online]. 2020, vol.101, n.2, pp.81-90. ISSN 1851-300X.

PityriasisRubra Pilaris is a papulosquamous disease, secondary to a cornification disorder of unknown cause, clinically manifested by hyperkeratosic papules and palmoplantar keratoderma. There are different ways to classify the disease, it corresponds to six subtypes depending on the age of onset, morphology, clinical course and prognosis. The most frequent form of presentation corresponds to the classic one of the adult (Type I), around 55% of all cases. Due to it is a low incidence disease, with an unclear etiology and the possibility of spontaneous remission, there is no universally accepted treatment and most of the evidence comes from individual case reports, small case series, and some retrospective studies. We present the clinical case of a 57-year-old patient diagnosed with PityriasisRubra Pilaris with a favorable response to retinoids.

Keywords : PityriasisRubra Pilaris; PityriasisRubra Pilaris adult classic.