Abstract

MARTINEZ, M et al. Acrokeratoelastoidosis: reportof a clinical case. Rev. argent. dermatol. [online]. 2021, vol.102, n.3, pp.1-8. ISSN 1851-300X.

Acrokeratolastoidosis is a rare genodermatosis of dominant autosomal, familial or sporadic inheritance, the latter being the most frequently reported form in the literature. It was described by the Brazilian dermatologist Oswaldo Costa in 1953. It is characterized by the presence of multiple hyperkeratotic papules, usually asymptomatic, located in the marginal area of the hands, feet or both. It usually begins in childhood, adolescence or early adult life and has a chronic course. Its differential diagnosis with the rest of the acrokeratosis is a great challenge, being the histological finding of elastorrexis the primary for its correct diagnosis. We present the case of a 22-year-old woman with a clinical and histopathology compatible with Acroqueratoelastoidosis.

Keywords : Acrokeratoelastoidosis; genodermatosis; keratoderma; hyperkeratotic papules; elastorrhexis.

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