Abstract

SOUSA MATIAS, Diego Alejandro; GONZALEZ, Alejandra  and  IDOYAGA, Pablo. Interstitial Lung Disease in Primary Biliary Cholangitis. Rev. am. med. respir. [online]. 2023, vol.23, n.3, pp.248-251. ISSN 1852-236X.  http://dx.doi.org/10.56538/ramr.izkd7855.

During the course of PBC, interstitial lung involvement may develop: organizing pneumonia, interstitial fibrosis, lymphoid interstitial pneumonia, or non-specific interstitial pneumonia. Although the diagnosis of PBC usually precedes pulmonary manifestations, the opposite can occur. The frequency of interstitial disease in patients with PBC is not exactly known. It may or may not be associated with other connective tissue diseases; therefore, it is necessary to carry out a systematic search of these diseases and the pulmonary manifestations of this entity. We present the case of a patient with a previous diagnosis of PBC, who developed interstitial lung involvement during the course of the disease.

Keywords : Primary biliary cholangitis; Interstitial lung disease; Crazy paving.

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