Abstract

NUNEZ ALVARADO, Luis E; MORALES VASQUEZ, Edgar  and  MACCHIAVELLO FALCON, Raúl. Cifoescoliosis severa secundaria a neurofibromatosis. Presentación de un caso. Rev. Asoc. Argent. Ortop. Traumatol. [online]. 2020, vol.85, n.4, pp.393-402. ISSN 1852-7434.  http://dx.doi.org/https://doi.org/10.15417/issn.1852-7434.2020.85.4.1015.

Dystrophic scoliosis in neurofibromatosis is identifiable by being an acuteangle kyphoscoliosis involving a short segment of the spine and producing severe deformity that when associated with the dystrophic changes of the spine result in real surgical challenges. We report the clinical case of a 15-year male with severe dystrophic kyphoscoliosis at the thoracolumbar area, with apex at T9, scoliosis with a Cobb angle of 107 °, and segmental kyphosis of 110.7°. The patient underwent a three-stage surgery, performed through a posterior approach, involving a vertebral column resection (VCR) and titanium mesh replacement, and achieving a kyphosis correction of 56% and a scoliosis correction of 59.8%. The patient experienced no major complications nor sequelae and had a favorable course. The VCR is a powerful and demanding surgical technique that allows for the management of the complex kyphoscoliosis deformity to achieve spinal balance; however, it is not without complications, especially neurological and pulmonary complications, which may be unavoidable. Our patient’s quality of life has improved significantly.

Keywords : Neurofibromatosis; scoliosis; resection; spine.

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