Abstract

CULLARI, Leonardo M. et al. Tumor mesenquimático fosfatúrico de pelvis: abordaje multidisciplinario. Rev. Asoc. Argent. Ortop. Traumatol. [online]. 2022, vol.87, n.3, pp.360-370. ISSN 1852-7434.  http://dx.doi.org/https://doi.org/10.15417/issn.1852-7434.2022.87.3.1371.

Phosphaturic mesenchymal tumor (PMT) is an infrequent clinicopathological entity. It presents insidious bone pain and polymyalgia, accompanied by alterations in calcium and phosphorus metabolism that are difficult to resolve clinically. A multidisciplinary approach is a key to success in this pathology. We present the case of a 52-year-old female patient with a 10-year history of PMT in the right hemipelvis with ipsilateral hip extension. From the clinical point of view, she presented oncogenic osteomalacia (hypophosphatemia and hyperphosphaturia) that did not correct despite being administered the latest generation medication, burosumab, an FGF-23 inhibitor that increases renal tubular phosphate reabsorption. Resection with oncological margins was decided by a multidisciplinary committee resolving her clinical condition. Due to the rarity of this pathology, we decided to report the case.

Keywords : Phosphaturic mesenchymal tumor; oncogenic osteomalacia; oncological orthopedics; pelvic surgery.

        · abstract in Spanish     · text in Spanish     · Spanish ( pdf )