Abstract

TERC TELIAS, F; MEZA FABIA, E; SEGOVIA GONZALEZ, L  and  CHAVEZ ROJAS, F. Chronic late-onset intertriginous dermatitis: Hailey-Hailey's pemphigus. Rev. argent. dermatol. [online]. 2017, vol.98, n.1, pp.21-26. ISSN 1851-300X.

The benign familial pemphigus or Hailey Hailey´s disease is a rare autosomal dominant disorder. We present the clinical case of a patient with a five years history, characterized by vesicular intertriginous malodorous lesions with poor response to topical antifungal therapy. Skin biopsy it was compatible with Hailey Hailey´s disease which was managed with antibiotic therapy and systemic corticosteroids. The patient evolved favorably.

Keywords : genodermatosis; benign familial pemphigus; Hailey Hailey's disease; intertrigo.