Resumo

GONZALEZ GARCIA, Gonzalo; BRETON HERNANDEZ, Patricia; BOILLOS CALVO, María J  e  MIRALLES PUIGBERT, Anna. Transverse vaginal septum diagnosed in sisters: Cases report. Arch. argent. pediatr. [online]. 2017, vol.115, n.3, pp.e150-e152. ISSN 0325-0075.  http://dx.doi.org/10.5546/aap.2017.e150.

Transverse vaginal septum is a disorder that would arise from a failure in the fusion and/or channeling of the urogenital sinus and the müllerian ducts with low frequency but with a significant impact on the health of patients. The treatment is surgical and it will depend on the location and thickness of the septum. Sometimes, it described a female sex-limited autosomal recessive transmission but few cases of family association have been reported. We present the cases of two sisters who had this rare entity 5 years apart and were diagnosed by the presentation of an intense hypogastric abdominal pain at the age of 11 and 12 years when they had a Tanner stage III pubertal development and primary amenorrhea.

Palavras-chave : Transverse vaginal septum; M üllerian ducts abnormalities; Heredity; Hematocolpos; Abdominal pain.

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