Resumo

SANCHEZ ZAHONERO, Julia; RUIZ DOMINGUEZ, José A; SANCHEZ ZAHONERO, Sandra  e  JOSE LOPEZ GARCIA, M. A very rare cause of peripheral precocious puberty in a girl: ovarian sex cord tumor with annular tubules. Arch. argent. pediatr. [online]. 2017, vol.115, n.3, pp.e179-e182. ISSN 0325-0075.  http://dx.doi.org/10.5546/aap.2017.e179.

Sex cord tumor with annular tubules is an extremely uncommon gonadal stromal neoplasm. It represents 0.05-0.6% of all ovarian tumors, according to series. An unusual case is presented in a 6-year-old girl, detected as a result of an isosexual peripheral precocious puberty. The highlight of this case is that no mass attached to the ovary was found, but only a gonadal asymmetry without radiological signs of malignancy. After confirming the presence of tumoral cells by intraoperative biopsy, unilateral salpingo-oophorectomy with ipsilateral para-aortic and pelvic lymphadenectomy was performed. Afterwards, the evolution of the patient was favorable.

Palavras-chave : Sex cord-gonadal stromal tumors; Precocious puberty; Inhibin B.

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